hrp0097p2-213 | Adrenals and HPA Axis | ESPE2023

Pseudohypoaldosteronism in congenital anomaly of the kidneys and urinary tract – case presentation

Elkina Stanimira , Bozhanova Venetsiya , Halvadzhiyan Irina , Petrova Chayka

Introduction: Pseudohypoaldosteronism (PHA) is a clinical syndrome characterized by multiorgan or isolated renal tubular resistance to the effects of aldosterone, resulting in hyperkalemia, metabolic acidosis, and normal to high serum aldosterone levels. PHA may be primary (hereditary) or secondary (acquired). Primary forms are subclassified into two: PHA type 1 (salt-wasting) and PHA type 2 (salt-retaining). Secondary forms are typically associated with sever...